Isoleucine-, leucine- and valine-free powder for dietary management of children and adults (3 years and older) with Maple Syrup Urine Disease (MSUD) or other inborn errors of branched chain amino acid metabolism.
Indication
Isoleucine-, leucine- and valine-free powder for dietary management of children and adults (3 years and older) with Maple Syrup Urine Disease (MSUD) or other inborn errors of branched chain amino acid metabolism.
Product Forms
Product | Format | Unit Size | Approximate Product Yield at Normal Dilution | Shelf Life | Item Number |
---|---|---|---|---|---|
BCAD2 | Powder | 454 g | Yield Not Applicable to Metabolics | 24 Months | 1281386 |
Preparation Of Feedings
Mead Johnson BCAD 2 is to be used only in the dietary management of children and adults with documented maple syrup urine disease or other inborn errors of branched chain amino acid metabolism while under direct and continuing medical supervision.
WARNING: This product is nutritionally incomplete. Continuing medical supervision and frequent blood tests are required. BCAD 2 must be supplemented using other food sources of protein and fluid to provide enough isoleucine, leucine and valine to support dietary requirements of children and adults.
INSTRUCTIONS FOR PREPARATION AND USE
Your medical professional will provide the correct amount of powder to mix with water for consumption.*
It is important to follow the directions below.
Nutrients
Analysis | per 100 mL | per 100 g |
---|---|---|
Energy (kcal/kJ) | 85/360 | 410/1720 |
Protein equivalent (g) | 5 | 24 |
% of total energy | 24 | 24 |
Source: Amino Acid Premix | ||
Carbohydrate (g) | 11.9 | 57 |
% of total energy | 57 | 57 |
Source: Corn syrup solids, sugar, modified corn starch | ||
Fat (g) | 1.77 | 8.5 |
% of total energy | 19 | 19 |
Source: Soy oil | ||
Linoleic Acid (g) | 0.87 | 4.2 |
Linolenic Acid (g) | 0.108 | 0.52 |
Minerals | ||
Calcium (mg) | 152 | 730 |
Calcium (mMol) | 3.8 | 18.2 |
Phosphorus (mg) | 152 | 730 |
Phosphorus (mMol) | 4.9 | 24 |
Magnesium (mg) | 34 | 163 |
Magnesium (mMol) | 1.39 | 6.7 |
Iron (mg) | 2.5 | 12.2 |
Zinc (mg) | 2.5 | 12.2 |
Manganese (mg) | 0.27 | 1.3 |
Copper (mg) | 0.25 | 1.22 |
Iodine (mg) | 0.0131 | 0.063 |
Selenium (mg) | 0.0058 | 0.028 |
Sodium (mg) | 127 | 610 |
Sodium (mMol) | 5.5 | 27 |
Potassium (mg) | 250 | 1220 |
Potassium(mMol) | 6.5 | 31 |
Chloride (mg) | 210 | 1020 |
Chloride (mMol) | 6 | 29 |
Vitamins | ||
Vitamin A (IU) | 360 | 1730 |
Vitamin D (IU) | 73 | 350 |
Vitamin E (IU) | 2.4 | 11.4 |
Vitamin K (mg) | 0.0098 | 0.047 |
Vitamin C (mg) | 11.9 | 57 |
Thiamine (mg) | 0.3 | 1.42 |
Riboflavin (mg) | 0.24 | 1.14 |
Niacin (mg) | 5.4 | 26 |
Pantothenic Acid (mg) | 1.19 | 5.7 |
Vitamin B6 (mg) | 0.24 | 1.14 |
Folic Acid (mg) | 0.085 | 0.41 |
Vitamin B12 (mg) | 0.00058 | 0.0028 |
Biotin (mg) | 0.0119 | 0.057 |
Choline (mg) | 20 | 98 |
Inositol (mg) | 11.9 | 57 |
Carnitine (mg) | 10.2 | 49 |
Taurine (mg) | 11.9 | 57 |
Other Characteristics | |
---|---|
Potential Renal Solute Load (mOsm/100 mL)1 | 51 |
Osmolality (mOsm/kg H2O)* | 900 |
Osmolarity (mOsm/L)* | 780 |
Water (g/100 mL) | 86 |
Ingredients
Corn Syrup Solids, Amino Acids (L-Glutamine, L-Lysine Hydro - Chloride, Potassium Aspartate, L-Proline, L-Alanine, L-Arginine, L-Phenylalanine, L-Tyrosine, L- Threonine, L-Serine, Glycine, L-Histidine, L-Methionine, L-Tryptophan, L-Cystine), Sugar, Soy Oil, Modified Corn Starch, Calcium Phosphate, And Less Than 1%: Sodium Citrate, Magnesium Phosphate, Potassium Chloride, Sodium Phosphate, Potassium Citrate, Choline Chloride, Ascorbic Acid, Taurine, Inositol, Ferrous Sulfate, L-Carnitine, Zinc Sulfate, Niacinamide, Vitamin E Acetate, Vitamin A Palmitate, Calcium Pantothenate, Cupric Sulfate, Manganese Sulfate, Vitamin B12, Thiamin Hydrochloride, Vitamin B6 Hydrochloride, Riboflavin, Folic Acid, Vitamin D3, Chromic Chloride, Sodium Molybdate, Sodium Iodide, Biotin, Sodium Selenite, Vitamin K1, Ethyl Vanillin.